Diagnostic Criteria for Scleroderma Renal Crisis
1. New onset blood pressure >150/85 mm Hg OR increase 220 mm Hg from
usual systolic blood pressure.
2. A decline in renal function, defined as an increase in serum creatinine of >10 %
Supportive features:
- Microangiopathic hemolytic anemia
- Findings consistent with accelerated hypertension on retinal examination
- Microscopic hematuria on urine dipstick and/or red blood cells on urine microscopy
- Oliguria or anuria
- Flash pulmonary edema
- Renal biopsy with typical features of SRC including onion skin proliferation within the walls of intrarenal arteries and arterioles, fibrinoid necrosis, glomerular shrinkage
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