Vasculitis and Vasculitides
Large Vessel Vasculitis:
• Takayasu, Giant cell arteritis (GCA)
Medium Vessel Vasculitis:
• Polyarteritis Nodosa, Kawasaki Disease
Small Vessel Vasculitis:
• ANCA Associated: Microscopic Polyangiitis, Eosinophilic Granulomatosis with Polyangiitis (EGPA), Granulomatosis with Polyangiitis (GPA)
IMMUNE COMPLEX VASCULITIS: Henoch Schonlein Purpura (IgA vasculitis), AntiGBM, Cryoglobulinemic Vasculitis, Hypocomplementenemic Urticarial Vasculitis
• Others: Lupus Vasculitis, Drug associated, Levamisole associated, Hydralazine -induced ANCA-associated vasculitis
Variable-Vessel Vasculitis:
• Behcet syndrome, Cogan syndrome
Lab tests:
• CBC, LFT, ESR, ANA, Complement, Urinalysis, TSH, SPEP
• ANCA
- (C-ANCA) pattern antibodies directed against PR3
- (P-ANCA) pattern is usually directed against MPO
• Consider: Serologies for Cryoglobulins, HIV, HBV, HCV, ASO
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