Alkaptonuria (Black Urine Disease)
Urine turns dark ...
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Description

Alkaptonuria (Black Urine Disease)

Urine turns dark when left standing due to oxidation of homogentisic acid 

Clinical 

 • Usually asymptomatic in childhood 

 • Ochronotic arthritis (due to deposits) 

 • Calcification of multiple intervertebral discs 

Management 

 • No effective therapy is available 

 • Diet: limit tyrosine and phenylalanine 



#Alkaptonuria #BlackUrine #Peds #Pediatrics #Diagnosis #Pathophysiology
Contributed by

Dr. Gerald Diaz
@GeraldMD
Board Certified Internal Medicine Hospitalist, GrepMed Editor in Chief 🇵🇭 🇺🇸 - Sign up for an account to like, bookmark and upload images to contribute to our community platform. Follow us on IG:  https://www.instagram.com/grepmed/ | Twitter: https://twitter.com/grepmeded/
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