Description
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group
MONOCLONAL CRYOGLOBULINEMIA (TYPE 1)
IgM monoclonal component
• Target lymphoplasmacytic proliferation (CD20+)
• Rituximab, obinutuzumab, bendamustine, chloraminophene
IgG monoclonal component
• Target plasma cells (CD20-)
• Alkylating agents, bortezomib, thalidomide or lenalinomide
MIXED CRYOGLOBULINEMIA (TYPES II AND III)
Glucocorticoids Immunosuppressive or immunomodulatory agents if severe and/or refractory disease ± Plasma exchanges
Dr. Benjamin Terrier @ https://twitter.com/TerrierBen
#NonHCV #Cryoglobulinemia #Vasculitis #Management #Rheumatology #Monoclonal #Mixed #Cryoglobulinemic