Susac Syndrome - Clinical Triad
- Central nervous system dysfunction
- Branch retinal artery occlusion
- Sensorineural hearing impairment
Therapeutic strategy
1. Glucocorticoids + antiplatelet
2. Anticoagulants
3. Cyclophosphamide
4. IVIg
5. Rituximab
Evolution
Acute phase
- Recurrent disease flares
- 2-year time period
Late phase
- Neurological/ENT remission
- Recurrent leakage of fluorescein from retinal arterioles
- Treatment ?
By Dr. Clémence David
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