Susac Syndrome - Clinical Triad
 - Central nervous ...
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Description

Susac Syndrome - Clinical Triad

 - Central nervous system dysfunction

 - Branch retinal artery occlusion

 - Sensorineural hearing impairment



Therapeutic strategy

1. Glucocorticoids + antiplatelet

2. Anticoagulants

3. Cyclophosphamide

4. IVIg

5. Rituximab



Evolution

Acute phase

 - Recurrent disease flares

 - 2-year time period

Late phase

 - Neurological/ENT remission

 - Recurrent leakage of fluorescein from retinal arterioles

 - Treatment ?



By Dr. Clémence David



#Susac #Syndrome #SusacSyndrome #Triad #Diagnosis #Management #Rheumatology
Contributed by

Dr. Gerald Diaz
@GeraldMD
Board Certified Internal Medicine Hospitalist, GrepMed Editor in Chief 🇵🇭 🇺🇸 - Sign up for an account to like, bookmark and upload images to contribute to our community platform. Follow us on IG:  https://www.instagram.com/grepmed/ | Twitter: https://twitter.com/grepmeded/
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